关键词: 肠系膜, Kaposi型血管内皮瘤, 卡梅诺现象

Abstract: Kaposiform hemangioendothelioma(KHE)is a vascular tumor characterized by intermediate malignancy.Retrospective analysis and literature review on the clinical pathologic,immunohistochemical and clinical data of a patient with mesentery KHE.The cardinal symptom of this patient is alimentary track hemorrhage,imageological diagnosed as a huge soft tissue mass of mesentery and invaded ileum.Clinical feature is without Kasabach-Merritt phenomenon,observing under the light microscope.The tumor is with cavernous vascular structure,and lymphocyte infiltration inside of stroma.The nodules are composed of disposed and lots of short spindle cell tumor;the tumor cells inside of the nodules are vertical and horizontal staggered and form tendon like or fissuring vessels.Immunohistochemistry:CD31(+),CD34(+),D2-40(+),C-Kit(-),SMA(-),Ki-67(1%).

Key words: Mesentery, Kaposiform hemangioendothelioma, Kasabach-merritt phenomenon(KMP)